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Pierre Robin Syndrome

What is Pierre Robin Syndrome?

Pierre Robin Syndrome is a congenital birth defect characterized by a smaller than normal lower jaw (micrognathia), with a tongue that tends to be displaced towards the throat. As a result, affected children tend to have breathing and eating difficulties. Currently, the exact cause of Pierre robin syndrome is still unknown, but interference during fetal development causes the baby's lower jaw to develop slowly before birth. When the lower jaw develops at a slower rate than the tongue, the closure of the palate is blocked and cleft palate develops, which explains why most of them also have cleft palate. For mild cases, this condition can self-correct as the lower jaw tends to grow rapidly to a normal size during the first year of life. In more severe cases, treatments, such as distraction osteogenesis or tracheostomy can be done to prevent the tongue from causing airway obstruction. If they also have eating difficulties, a gastrostomy tube can be used to feed food through the nose.

What are the Signs and Symptoms of Pierre Robin Syndrome?

Signs and symptoms of Pierre Robin Syndrome may include:

What Causes Pierre Robin Syndrome?

The cause of Pierre Robin Syndrome is not known or still under medical review.

What Increases the Risk of Pierre Robin Syndrome?

The risk of Pierre Robin Syndrome increases when you/your:

What Complications Can Pierre Robin Syndrome Cause?

Pierre Robin Syndrome may result in the following complications:

How Can You Prevent Pierre Robin Syndrome?

No specific prevention guideline exists for Pierre Robin Syndrome at this moment.

What Treatments are Available for Pierre Robin Syndrome?

Treatments and management of Pierre Robin Syndrome may vary depending on the individual patient and the severity of the medical condition. Treatment options may include:

  • Distraction Osteogenesis
  • Mandibular Sagittal Split Osteotomy
  • Maxillary Le Fort Osteotomy
  • Millard Procedure
  • Nasoalveolar Molding
  • Orthognathic Surgery
  • Percutaneous Endoscopic Gastrostomy
  • Tracheostomy
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